Familial pancreatic enzyme insufficiency.

نویسندگان

  • G Owen
  • P W Buss
  • H R Jenkins
  • A H Goodwin
  • M C Goodchild
چکیده

A father and son with profound reduction of exocrine pancreatic activity and little visible pancreatic tissue on ultrasound or computed tomography are described. Both have some degree of liver disease, which is more marked in the son. The disorder, apparently familial, does not correspond to any reported previously.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 67 12  شماره 

صفحات  -

تاریخ انتشار 1992